Characteristic | value | Characteristic | value |
---|---|---|---|
Gender (Number of patients (%)) | Scores | ||
Male | 85 (51.5%) | QMG modified (value ± SD) | 0.49 ± 0.4 |
Female | 80 (48.5%) | Female | 0.56 ± 0.4 |
Age at symptom onset (years ± SD) | 54.4 ± 19.3 | Male | 0.42 ± 0.3 |
Female | 50.1 ± 20.8 | Missing data (number of patients) | 0 |
Male | 58.4 ± 17.0 | ||
Age at diagnosis (years ± SD) | 55.4 ± 18.9 | MG-ADL (value ± SD) | 3.99 ± 3.5 |
Female | 51.9 ± 20.2 | Female | 4.8 ± 3.7 |
Male | 58.7 ± 17.1 | Male | 3.0 ± 3.0 |
BMI (kg/m2 ± SD) | 28.0 ± 5.5 | Missing data (number of patients) | 110 |
Female | 27.0 ± 5.8 | ||
Male | 29.1 ± 5.0 | MG-QoL15 (value ± SD) | 16.7 ± 13.0 |
Missing data (number of patients) | 41 | Female | 19.7 ± 12.4 |
Male | 13.0 ± 13.0 | ||
MGFA (number of patients (%)) | Missing data (number of patients) | 101 | |
I | 18 (10.9%) | ||
II | 70 (42.4%) | Treatment (number of patients (%)) | |
IIA | 34 (20.6%) | Pyridostigmine | 164 (99.4%) |
IIB | 14 (8.5%) | Pyridostigmine extended release | 139 (84.2%) |
Not class. | 22(13.3%) | Glucocorticosteroids | 143 (86.7% |
III | 31 (18.8%) | IVIG | 44 (26.7%) |
IIIA | 17 (10.3%) | AZA | 120 (72.7%) |
IIIB | 10 (6.1%) | MMF | 47 (28.5%) |
Not class. | 4 (2.4%) | Thymectomy (number of patients (%)) | 52 (31.5%) |
IV | 27 (16.4%) | ||
IVA | 2 (1.2%) | Thymoma | 17 (37.8%) |
IVB | 24 (14.5%) | Thymic hyperplasia | 12 (26.7%) |
Not class. | 1 (0.6%) | No pathology | 16 (35.6) |
V | 19 (11.5%) | Myasthenic crisis in the past | |
Serological status (number of patients (%)) | (number of patients (%)) | ||
No | 123 (74.5%) | ||
Anti-AChR-AB (+) (missing data n = 1) | 137 (83.5%) | Yes | 42 (25.5%) |
Anti-MuSK-AB (+) (missing data n = 75) | 5 (5.6%) | - 1 crisis | 29 (17.6%) |
Anti-Titin-AB (+) (missing data n = 63) | 36 (35.3%) | - 2 crisis | 5 (3.0%) |
Anti-LRP4-AB (+) (missing data n = 161) | 0 (0%) | - > 2 crisis | 8 (4.8%) |