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Table 3 BAEPs responses for the whole group (units in msec)

From: Abnormal auditory pathways in PHOX2B mutation positive congenital central hypoventilation syndrome

 

L A T E N C I E S

I N T E R P E A K S L A T E N C I E S

Patient n°

I

II

III

IV

V

III-I

V-III

V-I

 

R

L

R

L

R

L

R

L

R

L

R

L

R

L

R

L

1

1.7

1.6

3

3

4.4

4.5

5.8

5.7

6.6

6.5

2.7

2.9

2.2

2

4.9

4.9

2* #

2.3

1.8

/

/

4.7

/

/

/

/

7.2

2.4

/

/

/

/

5.4

3*

2.1

2.2

3

4.7

4.1

6.5

5.4

/

6.3

/

2

4.3

2.2

/

4.2

/

4*

2.2

2

3.3

/

4.6

4.4

/

/

6.6

6.6

2.4

2.4

2

2.2

4.4

4.6

5

1.8

1.8

2.6

2.7

3.9

3.8

5.1

5.3

5.8

5.9

2.1

2

1.9

2.1

4

4.1

6 #

2.3

2.5

3.2

3.5

4.5

4.6

5.9

5.8

6.3

6.4

2.2

2.1

1.8

1.8

4

3.9

7

2.2

2.2

3

3.4

4.2

4.4

5.2

5.6

6.3

6.3

2

2.2

2.1

1.9

4.1

4.1

8

1.4

1.3

2.7

2.4

3.6

3.4

4.9

4.6

5.7

5.3

2.2

2.1

2.1

1.9

4.3

4

9

1.6

1.7

2.7

2.8

3.9

4

4.8

5.1

5.7

5.9

2.3

2.3

1.8

1.9

4.1

4.2

10

1.9

2

2.6

2.7

3.7

3.8

4.7

4.7

5.7

5.7

1.8

1.8

2

1.9

3.8

3.7

11 #

2.5

2.3

/

/

4.1

4.2

4.9

5.4

6.1

6.1

1.6

1.9

2

1.9

3.6

3.8

12

1.7

1.8

2.9

2.8

3.9

3.9

5.3

5.2

5.8

5.9

2.2

2.1

1.9

2

4.1

4.1

13

1.7

1.6

2.8

2.8

3.8

3.8

5.2

5.1

5.8

5.7

2.1

2.2

2

1.9

4.1

4.1

14 #

2.5

1.9

/

3

/

4.1

/

5.8

/

6.2

/

2.2

/

2.1

/

4.3

15

1.6

1.7

2.9

2.7

3.8

3.8

5

5

5.9

5.8

2.2

2.1

2.1

2

4.3

4.1

  1. Abnormal BAEPs were found in 6 patients. *Brainstem dysfunction. # Peripheral auditory dysfunction.