Table 4 Summary of neuropsychological data in patients with Kii ALS/PDC and other types of dementia

MMSE total score (/30)

19.2 ± 6.4

22.7 ± 1.2*

23.2 ± 2.5*

22.0 ± 4.5

20.7 ± 1.3

Orientation (/10)

5.8 ± 3.3

7.9 ± 0.6*

8.0 ± 1.8

8.0 ± 0.6*

6.8 ± 1.6

Registration (/3)

2.9 ± 0.3

3.0 ± 0.0

3.0 ± 0.0

3.0 ± 0.0

3.0 ± 0.0

Attention and calculation (/5)

1.8 ± 1.9

2.1 ± 1.5

1.6 ± 0.9

1.7 ± 1.4

1.5 ± 1.1

Recall (/3)

0.6 ± 0.9

1.1 ± 0.7

2.1 ± 1.0*

1.9 ± 0.9*

1.2 ± 1.1*

Language and praxis (/9)

7.9 ± 1.2

8.2 ± 1.1

8.5 ± 1.1

7.9 ± 0.9

8.1 ± 1.1

RCPM

 Total score (/36)

19.3 ± 6.8

22.3 ± 6.2

21.2 ± 4.1

22.0 ± 4.4

19.3 ± 6.8

 Time (min sec)

14 37 ± 10 19

9 45 ±5 19*

12 56 ± 9 38

9 22 ± 3 51*

12 52 ± 6 39

Verbal fluency

 Semantic category

7.6 ± 3.2

8.5 ± 2.7

6.4 ± 2.9

7.8 ± 3.2

9.1 ± 3.2

 Letter category

3.6 ± 2.0

6.9 ± 2.1*

5.1 ± 2.6

4.5 ± 2.2

4.4 ± 1.7

PAWLT (/10)

5.0 ± 3.2

5.4 ± 1.9

7.1 ± 1.6*

6.0 ± 2.8

6.5 ± 3.5

FAB (/18)

8.0 ± 5.5

13.9 ± 6.0*

12.0 ± 2.2

10.0 ± 2.2

12.3 ± 2.6

(9 of 13 patients)

(8 of 12)

(4 of 10)

(4 of 10)

(3 of 10)