Variables | Non-survival group | Survival group | P values |
---|---|---|---|
No. of patients (%) | 32(17.0) | 156(83.0) | Â |
Sex, no. (%) | Â | Â | Â |
   Male: female ratio | 01:01.9 | 01:02.1 | 0.837 |
Classification of diagnosis | Â | Â | Â |
   PM | 5(15.6) | 37(23.7) | 0.363 |
   DM | 20(62.5) | 80(51.3) | 0.331 |
   ADM | 4(12.5) | 9(5.8) | 0.241 |
   OM | 2(6.25) | 24(15.4) | 0.261 |
   JM | 1(3.13) | 6(3.9) | 1 |
Mean age ± S.D at onset (year) | 52.9 ± 15.8 | 41.9 ± 15.2 | 0 |
Disease duration from onset to diagnosis, median (IQR) year | 3.8(2, 12.8) | 6.5(3, 12) | 0.215 |
Skin ulcers, (%) | 6(18.8) | 15(9.6) | 0.212 |
Complicated with ILD at disease course, (%) | 17(53.1) | 75(48.1) | 0.558 |
Complicated with PAH at disease course, (%) | 3(9.4) | 17(10.9) | 1 |
Complicated with malignancy, (%)e | 7(21.9) | 4(2.6) | 0 |
Complicated with dysphagia at disease course, (%) | 8(25.0) | 67(42.9) | 0.074 |
Cardiac involvement at disease course, (%) | 17(53.1) | 47(30.1) | 0.023 |
Raynaud phenomenon at disease course, (%) | 4(12.5) | 25(16.0) | 0.79 |
Low TP level†at diagnosis, (%) | 10(31.3) | 24(2.6) | 0.044 |
Low ALB levels†at diagnosis, (%) | 16(50.0) | 46(29.5) | 0.038 |
Elevated IgG††at diagnosis, (%) | 8(25) | 47(30.1) | 0.672 |
Elevated IgA††at diagnosis, (%) | 9(28.1) | 25(15.4) | 0.122 |
Elevated IgM††at diagnosis, (%) | 5(15.6) | 20(12.8) | 0.775 |
Creatine kinase at initial visit in our center, median (IQR) | 260.5 (71.8, 1173.8) | 491.5 (83.3, 1613.5) | 0.489 |
Autoantibodies positive at disease course, (%) | Â | Â | Â |
   ANA positive | 16(50.0) | 85(54.5) | 0.699 |
   Anti-RNP positive | 4(12.5) | 13(8.3) | 0.497 |
   Anti-Jo-1 positive | 0(0.0) | 24(15.4) | 0.016 |
   Anti-SSA positive | 2(6.3) | 33(21.2) | 0.048 |
MYOACT global disease activity, 10-cm VAS score at disease onset | 6.21 ± 2.61 | 6.64 ± 2.60 | 0.408 |
MYOACT muscle disease activity, 10-cm VAS score at disease onset | 7.09 ± 1.34 | 6.91 ± 1.3 | 0.47 |
MYOACT, subscale VAS score > 0 at disease onset | Â | Â | Â |
   Constitutional | 25(78.1) | 129(82.7) | 0.614 |
   Cutaneous | 25(78.1) | 111(71.2) | 0.518 |
   Skeletal | 10(31.3) | 42(26.9) | 0.666 |
   Gastrointestinal | 9(28.1) | 57(36.5) | 0.421 |
   Pulmonary | 4(12.5) | 12(7.7) | 0.483 |
   Cardiac | 9(28.1) | 35(22.4) | 0.497 |